Congenital cystic adenomatoid malformation: Case report

Abstract

Congenital cystic adenomatoid malformation (CCAM) is characterized by disorganized, hamartomatous and adenomatoid proliferation of primary bronchiole and occurs with the frequency of 1/11000-1/35000. Histopathologically, there are three types of CCAM, differing in the number and size of the cysts. Usually, surgical management for the symptomatic cases and clinical follow up for the asymptomatic cases are recommended. In this article, a 35-week-old premature infant with CCAM presenting with respiratory distress on postnatal fifth day was reported. A mass covering the 2/3 of the right lung and pushing the mediastinum to the left was determined by the chest radiography and the thorax computerized tomography. When the infant was 12 days old, right upper lobectomy and right lower lobe posterobasal segmentectomy were performed. Histopathologic examination was consistent with CCAM type I. The postoperative period was uneventful. On account of this patient, the importance of early surgical treatment for the symptomatic cases with CCAM was emphasized. © 2010 by Türkiye Klinikleri.