Please use this identifier to cite or link to this item: https://hdl.handle.net/11499/10339
Title: Pachyonychia congenita type I with severe oral leukokeratosis
Authors: Kirzioglu, Z.
Erdoğan, Yıldırım
Keywords: Oral leukokeratosis
Oral manifestations
Pachyonychia congenita
Publisher: University of Dicle
Abstract: Pachyonychia Congenita (PC) is a rare autosomal dominant keratin disorder that affects a number of ectodermal structures including the nails and palmoplantar skin, and often involves the oral mucosa, tongue, larynx, teeth and hair. Clinical features are usually present at birth or early infancy. There are two main subtypes of PC. Fingernail thickening and oral keratosis are more common and severe in PC-1 and cystic lesions, hair abnormalities, natal teeth and pili torti are more common in PC-2. We report the case of a 6-year-old boy with PC-1 presenting with severe and painful oral leukokeratosis and extensive caries.
URI: https://hdl.handle.net/11499/10339
ISSN: 1309-100X
Appears in Collections:Diş Hekimliği Fakültesi Koleksiyonu
Scopus İndeksli Yayınlar Koleksiyonu / Scopus Indexed Publications Collection

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